A Rare Case of a Patient with Hypoplastic Left Heart Syndrome and Subsequent Congenital Long Qtc Syndrome

Putschoegl A, Moran AM and

Abstract

Hypoplastic left heart syndrome continues to be one of the most complicated and devastating of all the congenital heart defects. Despite advances in surgical palliation, patients continue to face a high percentage of morbidity and mortality. This syndrome can be associated with multiple other genetic conditions although we believe we have found the first case that is associated with a congenitally prolonged QTc. We will discuss this presentation and the importance of considering multiple syndromes in those with congenital heart disease.

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