Intimal Sarcoma of the Pulmonary Artery in a Patient with Lynch Syndrome

Case Report

Riccardo Gherli, Giovanni M

Abstract

Intimal sarcomas of the Pulmonary Artery (PAS) are uncommon and highly lethal tumors. Due to their nonspecific symptoms, are often misdiagnosed with a poor prognosis due to its extreme aggressiveness. In this report, we present a case of PAS in a patient with a history of surgically treated Lynch Syndrome. Clinical and morphological findings are presented.

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