"It Started as a Spot" Dermatofibrosarcoma Protuberans

Scott N*, Causey C, Hodder

Abstract

We present a case of Dermatofibrosarcoma Protuberans (DFSP); a locally invasive soft tissue sarcoma that arises in the dermis of the skin. DFSP often starts as an asymptomatic, slow growing, pigmented, indurated/nodular area of skin. At this stage DFSP can be confused with a dermatofibroma, keloid scar, epidermal cysts and melanoma amongst others. Phases of rapid growth and bleeding occur, which prompt patient presentation. Wide local excision is the treatment of choice with close follow up due to the risk of local recurrence, however, metastasis is rare.