Pancreatic pseudopapillary tumor in association with colonic polyposis

Fatemeh Farahmand, Maryam Shoa

Abstract

We present a case of a female patient with familial adenomatous polyposis (FAP) and a history of pseudopapillary pancreatic tumor two years earlier. FAP is accepted to be a rare precancerous syndrome characterized by hundreds to thousands of c olorectal adenomatous polyps with a variety of extraintestinal manifestations. Solid pseudopapi llary tumor (SPT) is an uncommon exocrine pancreatic neoplasm. This rare pancreatic tumor sho uld be suspected in FAP patients especially if the patient has abdominal complaints. The developme nt of two rare entities in the same patient may suggest an association and research for a certain g enetic basis might be indicated.