Undifferentiated Embryonic Liver Sarcoma with Situs Inversus Totalis, Polysplenia, and Patent Ductus Venosus

Jessica El-Asmar, Nader Hir

Abstract

Situs inversus totalis in the pediatric population is a rare laterality defect characterized by a complete mirror-image reversal of the normal anatomy. The association with hepatic malignancies has been rarely described in the literature. Because of the complex anatomy, multidisciplinary approach and adequate pre-operative planning are crucial in order to understand the hepatic anatomy.

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